Neonatal Repair of Left Pulmonary Artery Sling and Long Segment Tracheal Stenosis With a Slide Tracheoplasty
We present the case of a 2.8 kg baby born with Axial Mesodermal Disruption syndrome that encompasses features of Oculo-Auriculo-Vertebral spectrum disorder and VACTERL. OAV spectrum disorder is also known as Goldenhar. The patient was diagnosed with a left pulmonary artery sling, long segment tracheal stenosis, atrial septal defect and bilateral superior vena cavae. The patient underwent a colostomy immediately after birth due to an imperforate anus. Patient was also diagnosed with cleft palate, microtia, micrognathia and encephalocele. Patient then underwent a slide tracheoplasty with reimplantation of left pulmonary artery. Post operative course was uneventful. We acknowledge the assistance of Dr. Manning with the management of this patient.