Marfan Syndrome: Single-Stage Surgical Repair of Pectus Excavatum Combined With Mitral Valve Repair and David Procedure
mediaposted on 31.10.2017, 18:44 by Andres Obeso, Jehad Ramahi, Olivier Jegaden
A 29-year-old male with a known history of Marfan syndrome was referred to the authors’ institute for surgical assessment. Physical examination showed a severe symmetric pectus excavatum, with a Haller Index of 7.8. Preoperative workup included a transesophageal echocardiography that revealed severe mitral valve regurgitation due to bileaflet mitral valve prolapse and a 5 cm aortic root dilatation involving the sinuses of Valsalva. The aortic valve was tricuspid and no alterations in flow were observed. A single-stage surgical repair of pectus excavatum and congenital heart lesions was recommended.
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