posted on 2021-12-06, 16:28authored byJames Tweddell, Alan ODonnell
<p>This video will demonstrate Dr. James Tweddell's surgical
strategy in 2-month-old male with diagnosis of aortic atresia, hypoplastic
aortic arch, coarctation, large perimembranous VSD, mildly hypoplastic mitral
valve, normal biventricular size, and bilateral SVC (left SVC to CS).
Intraoperative finding of aberrant right subclavian artery originating from
descending thoracic aorta with retroesophageal course. Patient was palliated in
the neonatal period with branch PA bands. Ductal patency maintained with
prostaglandin infusion through to definitive surgical repair date.</p>
<p> </p>
<p>A redo median sternotomy and extensive dissection was
performed. The ascending aorta was 2mm in diameter. There was an anomalous
origin of the right subclavian artery from the proximal descending thoracic
aorta. The right carotid artery was isolated and anastomosed to a Gore-Tex tube
graft. Graft, LSVC, and IVC cannulated and CPB was initiated.</p>
<p> </p>
<p>Antegrade cerebral perfusion was initiated. Graft was sewn
onto the carotid artery distally enough so that proximal carotid could have the
right subclavian artery reimplanted into it. The anomalous right subclavian
artery was ligated at its origin with Prolene suture and divided distal to the
ligature. It was mobilized from behind the esophagus and trachea. The proximal
carotid artery was incised longitudinally along the inferior aspect and the
subclavian artery was then anastomosed to the carotid artery in an end-to-side
fashion.</p>
<p> </p>
<p>Branch PAs were de-banded and gently dilated, thus not requiring
patch augmentation.</p>
<p> </p>
<p>Ductus was divided. Isthmus was not divided due to absence
of posterior shelf. The descending aorta was mobilized, first three sets of
intercostal branches taken. Incision completed from divided ductus and
continued along underside of aortic arch and lateral ascending aorta. Cutback
made to the left of facing commissure in pulmonary root. Damus-Kaye-Stansel was
performed. Edge of thoracic aorta and left lateral ascending aorta were joined
together. Anterior arch reconstructed with pulmonary homograft.</p>
<p> </p>
<p>Secundum ASD was closed. Ventriculotomy performed in right
ventricular free wall and enlarged to 15mm. VSD was enlarged superiorly and
anteriorly. Pledget-supported sutures placed along inferior rim avoiding injury
to tricuspid valve and conduction system. Ends of row were run continuously to
complete baffle. Bovine pericardium was used to create LV-to-aorta baffle.</p>
<p> </p>
<p>RVOT was reconstructed with 11mm pulmonary homograft with
anterior hood of bovine pericardium for proximal securement of conduit to
ventriculotomy.</p>
<p> </p>
<p>Echo showed good biventricular function, no residual VSD or
ASD. There was trivial left and right AV valve regurgitation. There was no
LVOTO or obstruction through the RV-to-PA conduit.</p>