Cor Triatriatum Sinister With an Intact Interatrial Septum and a Decompressing Vein in a Toddler BinsalamahZiyad M. De LeonLuis E. KaneLauren C. HeinleJeffrey S. 2018 <p><strong>Objectives</strong></p><p>Cor triatriatum sinister is a very rare cardiac anomaly that may lead to pulmonary hypertension, right ventricular dilation, and eventually right heart failure.</p><div><p><strong>Methods</strong></p><p>The authors report a procedure performed for a toddler who was misdiagnosed with asthma as an infant. She had progressive respiratory symptoms and was found to have cor triatriatum sinister with a restrictive communication, decompressing vertical vein, severe tricuspid regurgitation, and severe right ventricular dysfunction.</p><p><strong>Results</strong></p><p>The surgical repair, shown in the video, was uneventful and the right ventricular function was normalized on follow-up echocardiograms.</p><p><strong>Conclusion</strong></p><p>To the authors' knowledge, this is the first report of cor triatriatum sinister with a restrictive fenestration, a decompressing vertical vein, an intact interatrial septum, and severe tricuspid regurgitation in a toddler. The treatment was successful as demonstrated by the follow-up echocardiograms, which show normalization of the ventricular function and pulmonary artery pressure.</p><p>This educational content was originally presented during the STSA 64th Annual Meeting. This content is published with the permission of the <a href="https://stsa.org/">STSA</a>. For more information on the STSA and its next Annual Meeting, please click <a href="http://stsa.org/annualmeeting/">here</a>.</p></div>